About 643 results

ALLMedicine™ Restrictive Cardiomyopathy Center

Research & Reviews  241 results

Structural and functional cardiac changes in endomyocardial fibrosis treated with endom...
Echocardiography (Mount Kisco, N.Y.); Gibson GT, Majure DT et. al.

Jul 24th, 2021 - Eosinophilic myocarditis, a rare and under-recognized disease process, occurs due to cytotoxic inflammation of the endomyocardium that over time may lead to a restrictive cardiomyopathy. We report clinical, multimodality imaging, and pathologic fi...

Terminal osseous dysplasia with pigmentary defects and cardiomyopathy caused by a novel...
American Journal of Medical Genetics. Part A; Rumping L, Wessels MW et. al.

Jul 14th, 2021 - Terminal osseous dysplasia with pigmentary defects (TODPD), also known as digitocutaneous dysplasia, is one of the X-linked filaminopathies caused by a variety of FLNA-variants. TODPD is characterized by skeletal defects, skin fibromata and dysmor...

Improving contemporary outcomes following heart transplantation for cardiac amyloidosis.
Journal of Cardiac Surgery; McGoldrick MT, Etchill EW et. al.

Jul 14th, 2021 - The incidence of systemic amyloidosis is rising, and there is a concomitant rise in heart transplant for an indication of cardiac amyloidosis. We utilized the Organ Procurement and Transplantation Network (OPTN) database to retrospectively assess ...

Wild-type TTR amyloidosis among patients with unexplained heart failure and systolic LV...
PloS One; Goland S, Volodarsky I et. al.

Jul 10th, 2021 - Transthyretin cardiac amyloidosis (ATTR-CA) is an increasingly recognized cause of heart failure (HF) with preserved left ventricular ejection fraction (LVEF), typically presenting as restrictive cardiomyopathy. The potential co-existence of ATTR-...

Cardiac Amyloidosis: Presentations, Diagnostic Work-up and Collaborative Approach for C...
Current Problems in Cardiology; Joury A, Gupta T et. al.

Jun 28th, 2021 - Cardiac amyloidosis is a systemic disease characterized by continuous deposition of misfolded proteins called amyloid fibrils in the extracellular space which result in restrictive cardiomyopathy. The most common form of cardiac amyloidosis is lig...

see more →

Clinicaltrials.gov  4 results

Novel Cardiac Magnetic Resonance Imaging to Define a Unique Restrictive Cardiomyopathy in Sickle Cell Disease

Jun 18th, 2019 - Sickle cell disease (SCD) causes progressive cardiopulmonary morbidity, beginning in childhood, which can ultimately be fatal. As a group, cardiopulmonary complications, such as acute chest syndrome and sudden death, are now the most common causes...

Genotype-Phenotype Associations in Pediatric Cardiomyopathy (PCM GENES)

May 1st, 2018 - Pediatric cardiomyopathy is a heterogeneous genetic disease with high morbidity and mortality in which children often present with fulminant disease leading to death or transplant. The long-term goal of this project is to identify the genetic basi...

Physiologic Assessment of Microvascular Function in Patients With Cardiac Amyloidosis

Jun 16th, 2016 - Amyloidosis is rare systemic disorder characterized by the extracellular deposition of misfolded protein in various organ system, including heart. Among the several types of amyloid fibrils, the light chain and transthyretin amyloid proteins most ...

Epidemiology of Idiopathic Dilated Cardiomyopathy (Washington, DC Dilated Cardiomyopathy Study)

May 13th, 2016 - BACKGROUND: Idiopathic dilated cardiomyopathy is an often fatal cause of heart failure in young adults which is characterized by dilatation of the ventricles, increased myocardial mass, and impairment of systolic function. Dilated cardiomyopathy i...

see more →

News  11 results

UK's World-first Paediatric Heart Transplant Technique

Feb 22nd, 2021 - Two UK hospitals have collaborated to expand the donation after circulatory death (DCD) heart transplant programme to children. Doctors behind the scheme said the world-first paediatric heart transplant technique, previously only available to adul...

Carpal Tunnel Syndrome: 'Red Flag' for Subsequent ATTR, Heart Failure

Jul 1st, 2019 - Carpal tunnel syndrome may be an early warning sign of amyloidosis and heart failure, a Danish study showed. Matched by age and sex to the general population, people who got carpal tunnel surgery had higher risks of developing amyloidosis (0.10% v...

How to tell constrictive pericarditis from mimickers
Cardiology News;

Feb 11th, 2015 - A patient with constrictive pericarditis will have enhanced ventricular interaction arising from the restraint imposed by a rigid, diseased pericardium. That’s crucial.

Pediatric VAD Moves Toward Destination Tx

Jan 26th, 2015 - For children with failing hearts, ventricular assist devices (VADs) aren't just a means to reach transplant anymore. Use is already expanding into permanent, destination therapy use as it has for adults, Paul A. Checchia, MD, explained at the Soci...

Risk of Death When Waiting for a Heart Varies Widely

Jan 30th, 2014 - Action Points The risk of dying within 90 days of being placed on a heart transplant wait-list was 10 times greater for patients with the most risk factors compared with those with the fewest, suggesting a need for revising the current heart alloc...

see more →

Patient Education  1 results see all →