About 830 results

ALLMedicine™ Restrictive Cardiomyopathy Center

Research & Reviews  297 results

Acute Mitral Regurgitation Due to Chordae Tendineae Rupture: A Rare Presentation of Car...
The American Journal of Case Reports; Aguilar-López R, Sánchez-Rodríguez CC et. al.

Jul 6th, 2022 - BACKGROUND In cardiac amyloidosis (CA), misfolded proteins deposit in the extracellular space of cardiac tissue. These deposits classically cause restrictive cardiomyopathy with diastolic dysfunction. Although there are at least 30 proteins known ...

Large and Small Animal Models of Heart Failure With Reduced Ejection Fraction.
Circulation Research; Pilz PM, Ward JE et. al.

Jun 10th, 2022 - Heart failure (HF) describes a heterogenous complex spectrum of pathological conditions that results in structural and functional remodeling leading to subsequent impairment of cardiac function, including either systolic dysfunction, diastolic dys...

Clinical genetic testing in four highly suspected pediatric restrictive cardiomyopathy ...
BMC Cardiovascular Disorders; Zheng M, Huang H et. al.

May 26th, 2022 - Restrictive cardiomyopathy (RCM) presents a high risk for sudden cardiac death in pediatric patients. Constrictive pericarditis (CP) exhibits a similar clinical presentation to RCM and requires differential diagnosis. While mutations of genes that...

Mechanical and interventional support for heart failure with preserved ejection fractio...
Artificial Organs; Gordon JS, Blazoski CM et. al.

May 18th, 2022 - Restrictive cardiomyopathy (RCM) and hypertrophic cardiomyopathy (HCM) are two disease processes that are known to progress to heart failure with preserved ejection fraction (HFpEF). Pharmacologic therapies for HFpEF have not improved patient outc...

Pre-existing Ab against vimentin leads to false-positive HLA Ab results in two pediatri...
Pediatric Transplantation; Bansal S, Franz BJ et. al.

May 6th, 2022 - HLA Ab analysis is carried out as a routine assay both pre- and post-heart transplantation to identify Abs directed against HLA with a focus post-transplant on those Abs that are donor-specific. While virtual crossmatching has decreased the requir...

see more →

Clinicaltrials.gov  13 results

Healthy-related Quality of Life and Physical Activity of Children With Cardiac Malformations

Dec 30th, 2021 - Advances in paediatric cardiology has improved the prognosis of children with inherited cardiac disorders. However, quality of life and physical activity have been scarcely analysed in children with inherited cardiac arrhythmia or inherited cardio...

Molecular Imaging of Primary Amyloid Cardiomyopathy

Sep 23rd, 2021 - Primary light chain amyloidosis (AL) is the most common systemic amyloidosis, resulting from a plasma cell dyscrasia, a hematological malignancy. It causes a restrictive cardiomyopathy (AL-CMP) in over 70% of individuals. AL-CMP is as lethal as st...

Placenta Accreta New Detection Procedure by Rapid Assessment of Serum BNP

Apr 28th, 2021 - The investigators will conduct a monocentric , prospective, observational study, including 60 pregnant women, with history of at least one previous uterine scar, and scheduled for cesarian delivery. The participants will be divided into 3 equal gr...

Analysis of the Evolution of SUVmax by Quantitative Analysis Method of Bisphosphonate Scintigraphy

Apr 26th, 2021 - Cardiac amyloidosis is a cause of restrictive cardiomyopathy with preserved ejection fraction associated with amyloid fibrils deposits in the myocardium. Two types of amyloid commonly infiltrate the heart: immunoglobulin light-chain amyloid (AL), ...

Prevalence and Significance of ATTR Aortic Valve Amyloidosis in Degenerative Aortic Stenosis

Nov 19th, 2020 - Cardiac amyloidosis is a restrictive cardiomyopathy with a potentially severe prognosis that can be life-threatening. It is linked in the vast majority of cases to a light chain deposition of immunoglobulin or transthyretin. Although myocardial in...

see more →

News  20 results

Bullous Amyloidosis Masquerading as Pseudoporphyria
Kavita Darji, MD, Niraj Butala, MD et. al.

Oct 6th, 2021 - Cutaneous amyloidosis encompasses a variety of clinical presentations. Primary localized cutaneous amyloidosis comprises lichen amyloidosis, macular amyloidosis, and nodular amyloidosis.

Heart Failure Clinical Practice Guidelines (ESC, 2021) 

Sep 3rd, 2021 - Clinical practice guidelines on the management of heart failure by the European Society of Cardiology (ESC) were published in August 2021 in the European Heart Journal.[1] HFpEF (heart failure with preserved ejection fraction) diagnosis requires e...

UK's World-first Paediatric Heart Transplant Technique

Feb 22nd, 2021 - Two UK hospitals have collaborated to expand the donation after circulatory death (DCD) heart transplant programme to children. Doctors behind the scheme said the world-first paediatric heart transplant technique, previously only available to adul...

High-Dose Tafamidis Boosts Survival in Transthyretin Amyloidosis Cardiomyopathy

Jun 9th, 2020 - Treatment with oral tafamidis at 80 mg/day provided a significantly greater survival benefit than dosing at 20 mg/day in patients with transthyretin amyloid cardiomyopathy in the long-term extension of the landmark ATTR-ACT trial, Thibaud Damy, MD...

Fast Five Quiz: Test Your Knowledge on Key Aspects of Heart Failure

Feb 7th, 2020 - Because of increased myocardial oxygen consumption and demand beyond a critical level, the following high-output states can precipitate the clinical presentation of heart failure: Profound anemia Thyrotoxicosis Myxedema Paget disease of bone Albri...

see more →

Patient Education  2 results see all →