About 183 results

ALLMedicine™ Degos Disease Center

Research & Reviews  70 results

Degos disease in a child presenting with acute renal failure.
Pediatric Dermatology; Ng PSM, Koh MJA

Nov 29th, 2022 - Degos disease, also termed malignant atrophic papulosis, is a rare systemic vaso-occlusive disorder, seldom reported in the pediatric population. The pathognomonic skin lesion in Degos disease is a papule with an atrophic porcelain-white center wi...

Inflammation and thrombo-occlusive vessel signalling in benign atrophic papulosis (Köhl...
Journal of the European Academy of Dermatology and Venere... Zouboulis CC, Theodoridis A et. al.

Jun 25th, 2022 - Although the merely cutaneous, benign form of the extremely rare disease atrophic papulosis (Köhlmeier-Degos disease) may occasionally develop into the systemic, malignant form with time, it is unclear whether it exhibits any systemic characterist...

Atrophic papulosis (Köhlmeier-Degos disease) revisited: a cross-sectional study on 105 ...
Journal of the European Academy of Dermatology and Venere... Kaleta KP, Jarienė V et. al.

May 26th, 2022 - Atrophic papulosis is a very rare vascular disease of unknown pathogenesis, mostly described by case reports. To assess demographic data and prognosis in patients with atrophic papulosis. A single-centre study was performed on a series of 105 pati...

Exploring the pathophysiologic basis of constrictive pericarditis of Kohlmeier Degos di...
Annals of Diagnostic Pathology; Magro C, Shapiro L

May 20th, 2022 - Kohlmeier-Degos Disease is a unique thrombotic microvascular and arteriopathic vasculopathy that is highly selective in the organs it targets. It invariably involves the skin and can be a purely cutaneous process. It affects both the microvasculat...

Gastrointestinal Kohlmeier-Degos disease: a narrative review.
Orphanet Journal of Rare Diseases; Sattler SS, Magro CM et. al.

Apr 22nd, 2022 - Kohlmeier-Degos (K-D) disease is a rare obliterative vasculopathy that can present as a benign cutaneous form or with potentially malignant systemic involvement. The gastrointestinal tract is most frequently involved in systemic disease and mortal...

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News  3 results

Progressive Axillary Hyperpigmentation
Spyros M. Siscos, MD, Jace Rickstrew, MD et. al.

Jul 7th, 2021 - The Diagnosis: Dowling-Degos Disease Histopathology demonstrated elongation of the epidermal rete ridges with increased basal pigmentation, suprapapillary epithelial thinning, dermal melanophages, and a mild lymphocytic infiltrate (Figure). Given.

Atrophic Lesions in a Pregnant Woman
Santana D. VanDyke, MD, Darren J. Guffey, MD et. al.

Jun 14th, 2021 - The Diagnosis: Degos Disease The pathophysiology of Degos disease (malignant atrophic papulosis) is unknown. 1 Histopathology demonstrates a wedge-shaped area of dermal necrosis with edema and mucin deposition extending from the papillary dermis to.

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