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About 1,038 results

ALLMedicine™ Protein-losing Enteropathy Center

Research & Reviews  517 results

Severe Lymphatic Disorder Resolved With MEK Inhibition in a Patient With Noonan Syndrom...
https://doi.org/10.1542/peds.2020-0167
Pediatrics Dori Y, Smith C et. al.

Nov 21st, 2020 - Noonan syndrome is a multiorgan system disorder mediated by genetic defects along the rat sarcoma-mitogen-activated protein kinase (RAS-MAPK) pathway known as RASopathies. It is the second most common syndromic cause of congenital heart disease an...

Technical modifications for transplant in the failing Fontan.
https://doi.org/10.1017/S104795112000414X
Cardiology in the Young; Gil-Jaurena JM, Pardo C et. al.

Nov 19th, 2020 - Heart transplant after Fontan completion poses a unique surgical challenge. Twenty patients are presented, stressing the technical hints performed in the five anastomoses to match the graft in the recipient. Data are collected from 20 Fontan patie...

Sjögren syndrome associated with protein-losing enteropathy: case-based review.
https://doi.org/10.1007/s10067-020-05487-5
Clinical Rheumatology; de Carvalho JF, Lerner A et. al.

Nov 4th, 2020 - The association between Sjögren's syndrome (SS) and protein-losing enteropathy (PLE) was scarcly reported. To analyze the clinical, therapeutic, and outcome characteristics of patients with SS and PLE and also to delineate the potential mechanisms...

Overlap of lymphatic dysplasia in Fontan-associated protein-losing enteropathy and Muco...
https://doi.org/10.1017/S1047951120003182
Cardiology in the Young; Meisner JK, Koblick S et. al.

Oct 5th, 2020 - Lymphatic vessel dysplasia is associated with Fontan-associated protein-losing enteropathy. Extra nodal non-Hodgkin lymphomas including mucosa-associated lymphoid tissue (MALT lymphoma) are associated with lymphatic vessel dysplasia. Here, we desc...

Higher Incidence of Protein-Losing Enteropathy in Patients with Single Systemic Right V...
https://doi.org/10.1007/s00246-020-02468-y
Pediatric Cardiology; Bernardi AM, Moses S et. al.

Sep 25th, 2020 - Patients with single ventricle congenital heart disease are at risk of unpredictable protein-losing enteropathy (PLE) after surgical palliation. Based on prior reports of physiologic differences for patients with single morphologic right versus le...

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Clinicaltrials.gov  517 results

Severe Lymphatic Disorder Resolved With MEK Inhibition in a Patient With Noonan Syndrom...
https://doi.org/10.1542/peds.2020-0167
Pediatrics Dori Y, Smith C et. al.

Nov 21st, 2020 - Noonan syndrome is a multiorgan system disorder mediated by genetic defects along the rat sarcoma-mitogen-activated protein kinase (RAS-MAPK) pathway known as RASopathies. It is the second most common syndromic cause of congenital heart disease an...

Technical modifications for transplant in the failing Fontan.
https://doi.org/10.1017/S104795112000414X
Cardiology in the Young; Gil-Jaurena JM, Pardo C et. al.

Nov 19th, 2020 - Heart transplant after Fontan completion poses a unique surgical challenge. Twenty patients are presented, stressing the technical hints performed in the five anastomoses to match the graft in the recipient. Data are collected from 20 Fontan patie...

Sjögren syndrome associated with protein-losing enteropathy: case-based review.
https://doi.org/10.1007/s10067-020-05487-5
Clinical Rheumatology; de Carvalho JF, Lerner A et. al.

Nov 4th, 2020 - The association between Sjögren's syndrome (SS) and protein-losing enteropathy (PLE) was scarcly reported. To analyze the clinical, therapeutic, and outcome characteristics of patients with SS and PLE and also to delineate the potential mechanisms...

Overlap of lymphatic dysplasia in Fontan-associated protein-losing enteropathy and Muco...
https://doi.org/10.1017/S1047951120003182
Cardiology in the Young; Meisner JK, Koblick S et. al.

Oct 5th, 2020 - Lymphatic vessel dysplasia is associated with Fontan-associated protein-losing enteropathy. Extra nodal non-Hodgkin lymphomas including mucosa-associated lymphoid tissue (MALT lymphoma) are associated with lymphatic vessel dysplasia. Here, we desc...

Higher Incidence of Protein-Losing Enteropathy in Patients with Single Systemic Right V...
https://doi.org/10.1007/s00246-020-02468-y
Pediatric Cardiology; Bernardi AM, Moses S et. al.

Sep 25th, 2020 - Patients with single ventricle congenital heart disease are at risk of unpredictable protein-losing enteropathy (PLE) after surgical palliation. Based on prior reports of physiologic differences for patients with single morphologic right versus le...

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News  4 results

What is your diagnosis? - September 2019
https://www.mdedge.com/gihepnews/article/206986/mixed-topics/what-your-diagnosis-september-2019?channel=27662
Obaidullah Aseem, MD, Daniel S. Childs, MD et. al.

Aug 26th, 2019 - Erosive protein-losing enteropathy secondary to disseminated histoplasmosis This patient was treated with amphotericin B and transitioned to oral itraconazole with frequent blood level monitoring to ensure absorption. His symptoms improved gradual.

January 2019 - What's your diagnosis?
https://www.mdedge.com/gihepnews/article/191820/mixed-topics/january-2019-whats-your-diagnosis
Jen-Wei Chou, MD, Ken-Sheng Cheng, MD et. al.

Jan 1st, 2019 - Primary intestinal lymphangiectasia Histologic examination shows chronic inflammation of the ileum characterized by increased lymphoplasma cell infiltration of lamina propria without malignancy. Moreover, marked dilatation of lymphatic ducts that.

What is your diagnosis? - January 2019
https://www.mdedge.com/gihepnews/article/191820/mixed-topics/what-your-diagnosis-january-2019
Jen-Wei Chou, MD, Ken-Sheng Cheng, MD et. al.

Jan 1st, 2019 - Primary intestinal lymphangiectasia Histologic examination shows chronic inflammation of the ileum characterized by increased lymphoplasma cell infiltration of lamina propria without malignancy. Moreover, marked dilatation of lymphatic ducts that.

Rare mutation identified in fatal enteropathy
https://www.mdedge.com/pediatrics/article/100023/gastroenterology/rare-mutation-identified-fatal-enteropathy
Bianca Nogrady

Jul 1st, 2015 - Whole exome sequencing of an infant who died at 5 months of severe protein-losing enteropathy has revealed a rare mutation in the plasmalemma vesicle–associated protein gene. The infant, who was from consanguineous parents, presented at 8 days of.

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