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About 518 results

ALLMedicine™ Auditory Neuropathy Center

Research & Reviews  206 results

Vestibular and radiological characteristics of children affected by unilateral auditory...
https://doi.org/10.1016/j.ijporl.2021.110967
International Journal of Pediatric Otorhinolaryngology; Laurent C, Fayad G et. al.

Nov 18th, 2021 - Auditory neuropathy spectrum disorders (ANSD) are defined by the association of a preserved outer hair cell function and an impaired auditory nerve neural response, and present mostly bilaterally. Unilateral ANSD are consequently only seldom descr...

Multiple Cases of Auditory Neuropathy Illuminate the Importance of Subcortical Neural S...
https://doi.org/10.1097/AUD.0000000000001122
Ear and Hearing; White-Schwoch T, Anderson S et. al.

Oct 8th, 2021 - The role of subcortical synchrony in speech-in-noise (SIN) recognition and the frequency-following response (FFR) was examined in multiple listeners with auditory neuropathy. Although an absent FFR has been documented in one listener with idiopath...

Resolution of auditory neuropathy spectrum disorder after shunt placement in a patient ...
https://doi.org/10.1016/j.amjoto.2021.103250
American Journal of Otolaryngology; Lyle W, Sajjad A et. al.

Oct 4th, 2021 - There have been previous case reports suggesting the resolution of both sensorineural hearing loss and retrocochlear involvement through the management of hydrocephalus with shunt placement. This is a case report of a patient with Auditory Neuropa...

Molecular and genetic characterization of a large Brazilian cohort presenting hearing l...
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Human Genetics; Batissoco AC, Pedroso-Campos V et. al.

Oct 3rd, 2021 - Hearing loss is one of the most common sensory defects, affecting 5.5% of the worldwide population and significantly impacting health and social life. It is mainly attributed to genetic causes, but their relative contribution reflects the geograph...

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Clinicaltrials.gov  1 results

Evaluation of a Cohort of Congenital Deep Deafness Patients and/or With Auditory Neuropathy, Looking for DFNB9
https://clinicaltrials.gov/ct2/show/NCT04202185

Aug 3rd, 2021 - ANAD is not a rare type of hearing loss. Nevertheless, its profile is heterogeneous and the pathology remain underdiagnosed. The investigators will screen all new patients with bilateral severe to profound HL, looking for DFNB9. They will analyse ...

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