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About 2,003 results

ALLMedicine™ Lymphangioleiomyomatosis Center

Research & Reviews  973 results

CT findings of pulmonary cysts.
https://doi.org/10.1016/j.crad.2021.02.015
Clinical Radiology; Arango-Díaz A, Martínez-de-Alegría-Alonso A et. al.

Mar 20th, 2021 - Pulmonary cysts are thin-walled radiolucent lesions that may appear in a variety of uncommon disorders known as diffuse cystic lung diseases (DCLD) that essentially includes lymphangioleiomyomatosis (LAM), Langerhans cell histiocytosis (LCH), lymp...

Pregnancy after the diagnosis of lymphangioleiomyomatosis (LAM).
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7972207
Orphanet Journal of Rare Diseases; Shen L, Xu W et. al.

Mar 18th, 2021 - Lymphangioleiomyomatosis (LAM) is a rare disease that almost exclusively affects women of reproductive age. Patients are warned of the increased risks if they become pregnant. However, information on pregnancy in patients after the diagnosis of LA...

Therapeutic targeting of DGKA-mediated macropinocytosis leads to phospholipid reprogram...
https://doi.org/10.1158/0008-5472.CAN-20-2218
Cancer Research; Kovalenko A, Sanin A et. al.

Feb 17th, 2021 - Lymphangioleiomyomatosis (LAM) is a rare destructive lung disease affecting primarily women and is the primary lung manifestation of tuberous sclerosis complex (TSC). In LAM, biallelic loss of TSC1/2 leads to hyperactivation of mTORC1 and inhibiti...

Ultra-Small Lung Cysts Impair Diffusion Without Obstructing Air Flow in Lymphangioleiom...
https://doi.org/10.1016/j.chest.2021.01.077
Chest Matthew BP, Hasani AM et. al.

Feb 7th, 2021 - Lymphangioleiomyomatosis (LAM) is a rare lung disease found primarily in women of childbearing age, characterized by the formation of air-filled cysts, which may be associated with reductions in lung function. An experimental, regional ultra-high ...

Initial presentation of lymphangioleiomyomatosis in third trimester of pregnancy.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7813302
BMJ Case Reports; Alkemade L, Berghuis MAT et. al.

Jan 19th, 2021 - Lymphangioleiomyomatosis (LAM) is a progressive cystic lung disease which mostly affects premenopausal women and could be exacerbated by pregnancy. Therefore, it is thought that oestrogen plays an important role in LAM pathogenesis. Here, a case o...

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Guidelines  5 results

Lymphangioleiomyomatosis Diagnosis and Management: High-Resolution Chest Computed Tomography...
http://www.thoracic.org/statements/resources/interstitial-lung-disease/lam-guideline-pt2.pdf
Nishant Gupta

Nov 14th, 2017 - For women who have cystic changes on high-resolution computed tomography of the chest characteristic of LAM, but who have no additional confirmatory features of LAM (i. e.

Official American Thoracic Society/Japanese Respiratory Society Clinical Practice Guide...
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5803656
American Journal of Respiratory and Critical Care Medicine; McCormack FX, Gupta N et. al.

Sep 15th, 2016 - Lymphangioleiomyomatosis (LAM) is a rare cystic lung disease that primarily affects women. The purpose of these guidelines is to provide recommendations for the diagnosis and treatment of LAM. Systematic reviews were performed to summarize evidenc...

Lymphangioleiomyomatosis Diagnosis and Management
http://www.thoracic.org/statements/resources/interstitial-lung-disease/lam-guideline.pdf
Francis X. McCormack

Sep 14th, 2016 - After considering the panel’s confidence in the estimated effects, the balance of desirable (i. e.

The ERS guidelines for LAM: trying a rationale approach to a rare disease.
https://doi.org/10.1016/j.rmed.2010.03.015
Respiratory Medicine; Johnson SR

May 10th, 2010 - Lymphangioleiomyomatosis (LAM) is a rare lung disease which predominantly affects young women. LAM is associated with much morbidity and can lead to respiratory failure and death unless lung transplantation is performed. There are no randomised tr...

European Respiratory Society guidelines for the diagnosis and management of lymphangiol...
https://doi.org/10.1183/09031936.00076209
The European Respiratory Journal; Johnson SR, Cordier JF et. al.

Jan 1st, 2010 - European Respiratory Society guidelines for the diagnosis and management of lymphangioleiomyomatosis.|2010|Johnson SR,Cordier JF,Lazor R,Cottin V,Costabel U,|complications,diagnosis,therapy,

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Clinicaltrials.gov  999 results

CT findings of pulmonary cysts.
https://doi.org/10.1016/j.crad.2021.02.015
Clinical Radiology; Arango-Díaz A, Martínez-de-Alegría-Alonso A et. al.

Mar 20th, 2021 - Pulmonary cysts are thin-walled radiolucent lesions that may appear in a variety of uncommon disorders known as diffuse cystic lung diseases (DCLD) that essentially includes lymphangioleiomyomatosis (LAM), Langerhans cell histiocytosis (LCH), lymp...

Pregnancy after the diagnosis of lymphangioleiomyomatosis (LAM).
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7972207
Orphanet Journal of Rare Diseases; Shen L, Xu W et. al.

Mar 18th, 2021 - Lymphangioleiomyomatosis (LAM) is a rare disease that almost exclusively affects women of reproductive age. Patients are warned of the increased risks if they become pregnant. However, information on pregnancy in patients after the diagnosis of LA...

Therapeutic targeting of DGKA-mediated macropinocytosis leads to phospholipid reprogram...
https://doi.org/10.1158/0008-5472.CAN-20-2218
Cancer Research; Kovalenko A, Sanin A et. al.

Feb 17th, 2021 - Lymphangioleiomyomatosis (LAM) is a rare destructive lung disease affecting primarily women and is the primary lung manifestation of tuberous sclerosis complex (TSC). In LAM, biallelic loss of TSC1/2 leads to hyperactivation of mTORC1 and inhibiti...

Ultra-Small Lung Cysts Impair Diffusion Without Obstructing Air Flow in Lymphangioleiom...
https://doi.org/10.1016/j.chest.2021.01.077
Chest Matthew BP, Hasani AM et. al.

Feb 7th, 2021 - Lymphangioleiomyomatosis (LAM) is a rare lung disease found primarily in women of childbearing age, characterized by the formation of air-filled cysts, which may be associated with reductions in lung function. An experimental, regional ultra-high ...

Initial presentation of lymphangioleiomyomatosis in third trimester of pregnancy.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7813302
BMJ Case Reports; Alkemade L, Berghuis MAT et. al.

Jan 19th, 2021 - Lymphangioleiomyomatosis (LAM) is a progressive cystic lung disease which mostly affects premenopausal women and could be exacerbated by pregnancy. Therefore, it is thought that oestrogen plays an important role in LAM pathogenesis. Here, a case o...

see more →

News  25 results

What is the diagnosis?
https://www.mdedge.com/gihepnews/article/197796/what-diagnosis
Sarah Melloul, MD, Mostafa El Hajjam, MD et. al.

Mar 29th, 2019 - Cystic and calcified PEComa of the ligamentum teres PEComas are tumors derived from epithelioid perivascular cells that typically coexpress smooth muscle and melanocytic markers. The family of PEComas includes angiomyolipoma, clear cell “sugar” tu.

What is your diagnosis? - April 2019
https://www.mdedge.com/gihepnews/article/197796/what-your-diagnosis-april-2019?channel=27662
Sarah Melloul, MD, Mostafa El Hajjam, MD et. al.

Mar 29th, 2019 - Cystic and calcified PEComa of the ligamentum teres PEComas are tumors derived from epithelioid perivascular cells that typically coexpress smooth muscle and melanocytic markers. The family of PEComas includes angiomyolipoma, clear cell “sugar” tu.

This Month in the Journal CHEST® Editor’s Picks
https://www.mdedge.com/chestphysician/article/158052/society-news/month-journal-chestr-editors-picks
Richard S. Irwin, MD, FCCP, MDedge News

Feb 6th, 2018 - Giants In Chest Medicine Professor Nan-shan Zhong, MD. By Wei-jie Guan.

A 20-Year-Old Woman With Flank Pain and Vomiting
https://reference.medscape.com/viewarticle/877714_5

Mar 27th, 2017 - In 2012, new criteria for the diagnosis of TSC were published by the International Tuberous Sclerosis Complex Consensus Conference.[13] They include the following 11 major and six minor features. The major features are as follows: Hypomelanotic ma...

Drug Approved for LAM Illustrates How Patient Organizations Can Partner With Researchers
https://www.mdedge.com/neurology/article/100400/rare-diseases/drug-approved-lam-illustrates-how-patient-organizations-can

Jun 11th, 2015 - On May 28, FDA approved Rapamune (sirolimus) as a treatment for LAM (lymphangioleiomyomatosis), a rare, progressive and potentially fatal lung disease that affects primarily women of childbearing age. It is the first treatment to be approved for L.

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Patient Education  1 results see all →